- self limiting hip disorder caused by a varying degree of ischemia and subsequent necrosis of the femoral head; 
            - avascular necrosis of nucleus of proximal femoral epiphysis, abnormal growth of the physis, and eventual remodeling of regenerated 
                  bone are the key features of this disorder; 
            - loss of blood supply to the epiphysis is thought to be the essential lesion; 
    - usually seen in 4 to 8 yr old boy with delayed skeletal maturity; 
    - male to female ratio: 4-5 to 1; 
    - rare in blacks; 
    - increased incidence with a positive family history, low birth wt, and abnormal pregnancy / delivery; 
    - upto 12% of cases are bilateral but will be at different stages & are asymmetric (vs. MED
    - ageis the key to the prognosis - after 8 yr represents poor prognosis; 

 








 

 

 

- Clinical Presentation: 
    - includes pain (often knee pain) effusion (from synovitis) & a limp; 
    - early phase: 
          - limited abduction of hip & limited internal rotation in both flexion & extension are seen; 
          - antalgic gait (due to pain); 
    - late phase: Trendelenburg gait; 



 

- Long Term Consequences: 
    - coxa magna 
    - coxa plana 
    - coxa breva 
    - hinged abduction: 
          - occurs when an enlarged femoral head is laterally extruded and impinges against the 
                  acetabular rim when the hip is abducted; 

 

 

 

       此症常發於四至八歲之間的男孩子.

 

症狀之出現為漸進性.病童有疼痛、跛行現象,沒有全身症狀.患側髖部活動受制.

 

         照骨盤X時.即可見到股骨頭變形、崩壞、移位現象.而髖臼本身在初期還是好好的.這足以與結核病或其他疾病區別.

 

         因為此症的原因並不清楚,所以也沒有好的預防方法.

 

治療須按病人發病年齡、現在年齡、壞死程度、是否有半脫位、關節活動度等來作決定.

 

        若病人年齡小於六歲.壞死小於一半時.多半不需治療.但若壞死超過一半.且有半脫位現象時.則需考慮外張支架治療.

 

發病年齡大於七歲.壞死超過一半.有半脫位現象時.最好以手術治療.可以得到較佳的結果.

 

        不管何種治療.其目標都希望股骨頭在癒合的過程中得到保護.不致變形.若變形或半脫位.將來都容易發生關節炎.

 

 

 

 

 

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